GSS Prion Disease: Understanding Gerstmann-Sträussler-Scheinker Syndrome
What is Gerstmann-Sträussler-Scheinker Syndrome (GSS)? Gerstmann-Sträussler-Scheinker syndrome (GSS) is a rare, inherited, and invariably fatal neurodegenerative disorder. It belongs to a group of diseases known as prion diseases, which are characterized by the misfolding of a normal cellular protein, PrPC, into an abnormal, infectious isoform, PrPSc. This misfolded protein accumulates in the brain, leading to … Read more
